Adult diagnosis of Swyer-James-Macleod syndrome: retrospective analysis of four cases.

نویسندگان

  • Hadice Selimoglu Sen
  • Mahsuk Taylan
  • Ozlem Abakay
  • Cengizhan Sezgi
  • Mehmet Guli Cetincakmak
چکیده

Swyer-James-Macleod syndrome (SJMS) is a rare constrictive bronchiolitis with air-flow obstruction and a decreased number and diameter of ipsilateral peripheral pulmonary vessels. This syndrome is characterized by unilateral hyperlucency on chest radiography. Computed tomography provides useful additional information. The diagnosis is usually made in childhood but sometimes occurs in adulthood. The disease often presents with dyspnea, decreased exercise tolerance, cough, hemoptysis, and recurrent pulmonary infections. SJMS may be confused with asthma or pulmonary embolism due to similar symptoms and may result in inappropriate therapy. This case series examined the clinical and imaging spectrum of four patients who were diagnosed with SJMS in adulthood.

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عنوان ژورنال:
  • Respiratory care

دوره 59 4  شماره 

صفحات  -

تاریخ انتشار 2014